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Kartagener's Syndrome: A Case Report


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1 INHS Asvini, Nanabhai Moos Marg, Navy Nagar, Colaba, Mumbai, Maharashtra - 400005, India
     

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Kartagener's Syndrome is a subgroup of primary ciliary dyskinesias (PCD) which is characterised by impairment of mucociliary clearance. It is a rare, autosomal recessive disorder characterised by triad of situs invertus, chronic sinusitis and bronchiectasis. We report a case of this rare entity. Need for early diagnosis, appropriate respiratory management and timely treatment of infertility in these patients constitutes comprehensive management.
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  • Kartagener's Syndrome: A Case Report

Abstract Views: 234  |  PDF Views: 0

Authors

R. Tyagi
INHS Asvini, Nanabhai Moos Marg, Navy Nagar, Colaba, Mumbai, Maharashtra - 400005, India
S. Sahu
INHS Asvini, Nanabhai Moos Marg, Navy Nagar, Colaba, Mumbai, Maharashtra - 400005, India

Abstract


Kartagener's Syndrome is a subgroup of primary ciliary dyskinesias (PCD) which is characterised by impairment of mucociliary clearance. It is a rare, autosomal recessive disorder characterised by triad of situs invertus, chronic sinusitis and bronchiectasis. We report a case of this rare entity. Need for early diagnosis, appropriate respiratory management and timely treatment of infertility in these patients constitutes comprehensive management.