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Authors
Affiliations
1 INHS Asvini, Nanabhai Moos Marg, Navy Nagar, Colaba, Mumbai, Maharashtra - 400005, IN
Source
The Indian Practitioner, Vol 68, No 4 (2015), Pagination: 38-39
Abstract
Kartagener's Syndrome is a subgroup of primary ciliary dyskinesias (PCD) which is characterised by impairment of mucociliary clearance. It is a rare, autosomal recessive disorder characterised by triad of situs invertus, chronic sinusitis and bronchiectasis. We report a case of this rare entity. Need for early diagnosis, appropriate respiratory management and timely treatment of infertility in these patients constitutes comprehensive management.