Embryonal Rhabdomyosarcoma as a Gingival Growth:A Rare Presentation
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Rhabdomyosarcoma (RMS) is a malignant tumor of striated muscle composed of neoplastic mesenchymal cells with varying degrees of cell differentiation. It accounts 60% of all soft-tissue sarcomas in children and only 2-5% in adults. Typical pediatric rhabdomyosarcoma variants like embryonal and alveolar sub-types are less frequently occur in adults. It has predilection for viscera followed by the head and neck region. RMS occurs in the head and neck region with 35% and 10-12% in the oral cavity. Establishment of the correct diagnosis and histological sub-type is of very importance in the treatment of this disease, because of the rarity of this neoplasm in the adult population the treatment is not uniform in the literature. Here we present case of embryonal rhabdomyosarcoma as a gingival growth in a 26-year-old female with clinical, radiological, histo-pathological and immunohistochemical aspects.
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- Ankita T, Kanika S, Pratap SA. Oral rhabdomyosarcoma: A review. J Clin Exp Dent. 2012; 4(5):e302–e3028. https://doi.org/10.4317/jced.50926. PMid:24455040. PMCid:PMC3892211
- Egas-Bejar, Huh. Rhabdomyosarcoma in adolescent and young adult patients: Current perspectives. Adolesc Health Med Ther. 2014:5. https://doi.org/10.1016/j.jpfa.2016.09.002
- Arul AJ, Verma S, Arul A, Verma R. Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity. J Nat Sc Biol Med. 2014; 5:222–225. https://doi.org/10.4103/09769668.127347. PMid:24678235. PMCid:PMC3961943
- Jayaram V, Jayachandran S, Bhaskar YH. Embryonal rhabdomyosarcoma of oral cavity with extensive osteolysis of the mandible - A rare case report. J Pierre Fauchard Acad (India Sect). 2016. https://doi.org/10.1016/j.jpfa.2016.09.002
- Ilson S, Paulo V, Enrique P, Loreto SM, Vanessa K et. al. Sinonasal alveolar rhabdomyosarcoma in an adult patient: A case report and review of the literature. Canc Therapy and Oncol Int J. 2017; 3(4):555619. https://doi.org/10.19080/CTOIJ.2017.03.555619
- Parviz D, Saeideh K. Oral Rhabdomyosarcoma: A Case Report. J Clin Exp Pathol. 2014; 4:161.
- Raman K, Arora H, Keerthilatha M, Suhas S. Rhabdomyosarcoma of the Mandible. Int J Oral-Med Sci. 2013; 12(3):204–208. https://doi.org/10.5466/ijoms.12.204
- Muni S, Smita D, Kumar GS. Alveolar rhabdomyosarcoma involving the jaws: A case report. J Oral Maxillofac Surg. 2000; 58:1062–1065. https://doi.org/10.1053/joms.2000.8754
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