Informatics Publishing Limited

R. Tyagi ¹, S. Sahu ¹

Affiliations
1 INHS Asvini, Nanabhai Moos Marg, Navy Nagar, Colaba, Mumbai, Maharashtra - 400005, IN

Abstract

Kartagener's Syndrome is a subgroup of primary ciliary dyskinesias (PCD) which is characterised by impairment of mucociliary clearance. It is a rare, autosomal recessive disorder characterised by triad of situs invertus, chronic sinusitis and bronchiectasis. We report a case of this rare entity. Need for early diagnosis, appropriate respiratory management and timely treatment of infertility in these patients constitutes comprehensive management.

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R. Tyagi ¹, P. Pande ¹, A. Trehan ¹, R. S. Negi ², V. Hande ³

Affiliations
1 Department of Pathology, INHS Asvini, Mumbai, IN
2 Department of Radiodiagnosis and Interventional Radiology, INHS Asvini, Mumbai, IN
3 INHS Asvini, Mumbai, IN

Abstract

Idiopathic chronic eosinophilic pneumonia is a rare disorder of unknown cause characterized by respiratory symptoms of more than 2 weeks, alveolar or blood eosinophilia, peripheral pulmonary infiltrates on imaging after exclusion of known cause of eosinophilic lung disease. It is a rare disorder and contributes 0-2.5% in different registries of Interstitial Lung disease. Links between asthma and idiopathic chronic eosinophilic pneumonia have also been described. We report a case of this rare entity.

Keywords

Eosinophilia, Idiopathic Chronic Eosinophilic Pneumonia, Migratory Opacities, Broncho Alveolar Lavage.

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