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A Case of Pleomorphic Variant of Embryonal Rhabdomyosarcoma in Skeletal Muscle - A Rare Case Report


Affiliations
  • Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Department of Pathology, Nashik, India
 

Embryonal Rhabdomyosarcoma (ERMS) is a malignant soft tissue tumour with phenotypical and biological features of embryonic skeletal muscle cells. It is rare in skeletal musculature of extremities and its pleomorphic variant is rare which is associated with worse outcome. Here we are discussing a case of three year old male child who has presented with recurrence of swelling in right gluteal region arising in gluteus maximus muscle who is a known case of Rhabdomyosarcoma (RMS) 1 year back at the same site. Patient was operated with wide local excision and underwent chemotherapy cycles.

Keywords

Embryonal, Pleomorphic, Rhabdomyosarcoma (RMS)
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  • A Case of Pleomorphic Variant of Embryonal Rhabdomyosarcoma in Skeletal Muscle - A Rare Case Report

Abstract Views: 353  |  PDF Views: 107

Authors

Shital Dharrao
, India
Preeti Bajaj
, India
S. V. Mahajan
, India

Abstract


Embryonal Rhabdomyosarcoma (ERMS) is a malignant soft tissue tumour with phenotypical and biological features of embryonic skeletal muscle cells. It is rare in skeletal musculature of extremities and its pleomorphic variant is rare which is associated with worse outcome. Here we are discussing a case of three year old male child who has presented with recurrence of swelling in right gluteal region arising in gluteus maximus muscle who is a known case of Rhabdomyosarcoma (RMS) 1 year back at the same site. Patient was operated with wide local excision and underwent chemotherapy cycles.

Keywords


Embryonal, Pleomorphic, Rhabdomyosarcoma (RMS)

References





DOI: https://doi.org/10.18311/mvpjms%2F2016%2Fv3%2Fi2%2F7683